IgG/IgA Pemphigus: Report of a Rare Variant of Atypical Pemphigus and a Review of the Literature
نویسندگان
چکیده
First described as a distint clinical entity in 1994, IgG/IgA pemphigus is a rare type of atypical pemphigus with a variety of clinical, histological, and immunological manifestations. Only 21 cases of this disease have been reported in the literature to date. We report a case of IgG/IgA pemphigus in a 54-year old female in which the diagnosis was delayed due to negative direct immunofluorescence results following two separate biopsies. The clinical and histological findings associated with this rare form of pemphigus will be discussed along with a review of the literature.
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Childhood Pemphigus: Report of 2 cases
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